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Proteolysis of Mutant Huntingtin Produces an Exon 1 Fragment That Accumulates as an Aggregated Protein in Neuronal Nuclei in Huntington Disease

Proteolysis of Mutant Huntingtin Produces an Exon 1 Fragment That Accumulates as an Aggregated Protein in Neuronal Nuclei in Huntington Disease

Landles, C.; Sathasivam, K.; Weiss, A.; Woodman, B.; Moffitt, H.; Finkbeiner, S.; Sun, B.; Gafni, J.; Ellerby, L. M.; Trottier, Y.; Richards, W. G.; Osmand, A.; Paganetti, P.; Bates, G. P.
  • 期刊名称Journal of Biological Chemistry
  • 作者Landles, C.; Sathasivam, K.; Weiss, A.; Woodman, B.; Moffitt, H.; Finkbeiner, S.; Sun, B.; Gafni, J.; Ellerby, L. M.; Trottier, Y.; Richards, W. G.; Osmand, A.; Paganetti, P.; Bates, G. P.
  • 卷第285卷
  • 期第12期
  • 印刷ISSN0021-9258
  • 电子ISSN1083-351X
  • 文件大小6748.92KB
  • 发表时间2010-03-19
  • DOI10.1074/jbc.M109.075028
  • 页码8808-8823
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